【罕见同时侵犯左右心房的原发性心脏嗜铬细胞瘤】嗜铬细胞瘤是来源于神经嵴的产生儿茶酚胺的肿瘤。原发性心脏嗜铬细胞瘤是极为罕见的,全世界目前见于文献报道的仅为100例左右,北京协和医院心外科去年1月份成功进行了一例心脏嗜铬细胞瘤切除手术,患者为中年女性,肿瘤同时侵犯左右心房,其MIBG闪烁扫描的结果正常,但奥曲肽显像结果异常。肿瘤在体外循环下被成功切除。该病例报告已经发表在著名心胸外科专业杂志AnnalsofThoracicSurgery上。本文中的图表和表格Fig1.(A)99m-Technetium-labeledhydrazinonicotinyl-Tyr3-octretidescintiscandemonstratedafocusofintenseuptakeonrightsideofheartsilhouette.(B)Contrast-enhancedcomputedtomographicscanillustratedtumor(arrow)overlyinginteratrialgroove.(LA=leftatrium;RA=rightatrium.)[p=30,2,center]Fig2.Coronaryangiogramdemonstratedatumorblushwith2feedingvessels(whitearrows)branchingfromleftcircumflexartery.[p=30,2,center][img=360,387]http://w2.iiyi.com/bbs/uploadimg/z1357871845zakx8bt8.jpg[/img][p=30,2,center]Fig3.Resectedcardiacpheochromocytoma.PrimaryCardiacPheochromocytomaInvolvingBothRightandLeftAtriaXingrongLiu,MD,QiMiao,MD,HengZhang,MD,ChaojiZhang,MD,LihuaCao,MD,GuotaoMa,MD,ZhengpeiZeng,MDPheochromocytomasarecatecholamine-producingparagangliomasderivedfromtheneuralcrest.Primarycardiacpheochromocytomaisextremelyrare.Wedescribeacaseofcardiacpheochromocytomainvolvingbothrightandleftatriainamiddle-agedwoman.Metaiodobenzylguanidine(MIBG)scintiscanresultswerenormal,butresultsfromanoctreotidescanwereabnormal.Thetumorwassuccessfullyresectedusingcardiopulmonarybypass(CPB)。
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的确是非常罕见的病例,学习了,**!!!